Giant exophytic dermatofibrosarcoma protuberans of the breast. A case report with the analysis of clinical and therapeutical issues

Dermatofibrosarcoma protuberans (DFSP) is a rare neoplasm characterized by a high rate of local recurrence and a low risk of metastases. Occurrence in the breast is extremely rare and requires an adequate preoperative diagnosis for a correct management. We report a case of a giant exophytic DFSP of the right breast in a young-aged woman. Radical mastectomy was carried out without clinical evidence of local recurrence after 2 years follow-up. Specific pathological features and recommendations for the clinical management are discussed.